A fatal presentation of dermatomyositis with facial swelling.

Feb 2012

Dwivedi N, Michael C, Lew DB, Arnold S, Igarashi M, Bertorini T, Thompson JW, Myers LK, Brown ML.

Source

Departments of Microbiology, Immunology and Biochemistry, University of Tennessee Health Science Center, Memphis, TN, 38163, United States.

Abstract

Juvenile dermatomyositis (JDM) is the most common inflammatory autoimmune myopathy in children. Most common presentations consist of heliotrophic rash and/or gottron's papules in addition to proximal muscle weakness. A typical presentations have been reported. We present a 13-year-old African American male who presented with a two-week history of bilateral periorbital edema that was unresponsive to glucocorticoids. He had elevated transaminases but no detectable muscle weakness. A muscle biopsy was consistent with juvenile dermatomyositis. This case highlights the need to consider dermatomyositis in cases of facial

PubMed